Creutzfeldt-Jakob Disease (CJD) Data

  •  The year a Creutzfeldt-Jakob disease (CJD) case is counted is based on the year of death.
Texas Creutzfeldt-Jakob Disease Case Counts by Type of Disease and Year (2012-2021)
Classifi-
cation
Trans-
mission 
Type
Disease Type 2012 2013 2014 2015 2016 2017 2018 2019 2020  2021  Total Counts
Confirmed Acquired vCJD                    1
Familial fCJD      3     1 2 4 3 14
FFI                    1
Sporadic sCJD  10  10  11  14 18  15  21 24 13  15 151 
sFI                    1
VPSPr  1       1       2 5
Probable Familial fCJD    1       1  
Sporadic sCJD  10 10 4 14 11 17  26 24 128
Possible  Sporadic sCJD        1         1 3
Total Counts 22 14  27 20  33 25  36 46 41  45 309

vCJD: variant Creutzfeldt-Jakob Disease; fCJD: familial Creutzfeldt-Jakob Disease; FFI: Fatal Familial Insomnia; sCJD: sporadic Creutzfeldt-Jakob Disease; sFI: sporadic Fatal Insomnia; VPSP: variably protease-sensitive prionopathy.   

Texas Creutzfeldt-Jakob Disease Deaths and Death Rates per Year (2012-2021)
Case Year Case Counts Case Rate per Million Population
2012 22  0.83
2013 14 0.52
2014 27 0.98
2015 20  0.72
2016 33  1.17
2017 25 0.87
2018 36  1.23 
2019 46 1.58
2020  41 1.38 
2021 45 1.49
Average 30.9 1.1

Average Number of Texas Cases (Deaths) per Year = 30.9
Average Rate of Cases (Deaths)/Million Population/10 years = 1.1

Population data for years 2012-2018 is from the Department of State Health Services, Center for Health Statistics. Population data for 2019-2021 is projected population from Texas Demographic Center’s Texas Populations Projections Program (https://demographics.texas.gov/data/tpepp/Projections/#srePop) and updated on July 18, 2019. For years 2012 (26,403,743), 2013 (26,932,619), 2014 (27,470,110), 2015 (27,695,284), 2016 (28,240,245), 2017 (28,797,290), 2018 (29,366,479), 2019 (29,193,268), 2020 (29,677,668), and 2021 (30,168,926), projected population was used.

Population data for years 2012-2018 is from the Department of State Health Services, Center for Health Statistics. Population data for 2019-2021 is projected population from Texas Demographic Center’s Texas Populations Projections Program (https://demographics.texas.gov/data/tpepp/Projections/#srePop) and updated on July 18, 2019. For years 2012 (26,403,743), 2013 (26,932,619), 2014 (27,470,110), 2015 (27,695,284), 2016 (28,240,245), 2017 (28,797,290), 2018 (29,366,479), 2019 (29,193,268), 2020 (29,677,668), and 2021 (30,168,926), projected population was used.

Creutzfeldt-Jakob Disease Case Counts by Gender and Year (2012-2021) 
Gender 2012 2013 2014 2015 2016 2017 2018 2019 2020 2021 Totals
Male 12 6 11 18  9 14 23 19  28 149
Female  10 16 11  15  16 22  23 22 17 160
Total Counts 22 14  27 20 33 25 36 46 41  45 309 
                       
Gender 2012 2013 2014 2015 2016 2017 2018 2019 2020 2021 Avg %
% Males 55% 43% 41% 45% 55% 36% 39% 50% 46% 62% 47% 
% Females 45% 57% 59% 55% 45% 64% 61% 50% 54% 38% 53%


Creutzfeldt-Jakob Disease Case Counts and Percentages by Year and Age Category (2012-2021)
Year <55 Years of Age % <55 Years of Age  55 Years of Age % ≥ 55 Years of Age Total Cases
2012 27% 16 73% 22
2013 1 7% 13 93% 14
2014 5 19% 22 81% 27
2015 2 10% 18 90% 20
2016 18% 27 82% 33
2017 3 12% 22 88% 25
2018 11% 32 89% 36
2019 4 9% 42 91% 46
2020 22%  32 78%  41
2021 1 2% 44 98% 45
Total  41 13% 268 87% 309

CJD21